:Papuloerythroderma of Ofuji

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Papuloerythroderma of Ofuji is a rare disorder most commonly found in Japan, characterized by pruritic papules that spare the skinfolds, producing bands of uninvolved cutis, creating the so-called deck-chair sign. Frequently there is associated blood eosinophilia. Skin biopsies reveal a dense lymphohistiocytic infiltrate, eosinophils in the papillary dermis, and increased Langerhans cells (S-100 positive). Systemic steroids are the treatment of choice and may result in long-term remissions.{{cite book | vauthors = James WD, Berger TG, Elston DM |year=2005 |title=Andrews' Diseases of the Skin: Clinical Dermatology |edition=10th |publisher=Saunders |isbn=978-0-7216-2921-6 |page=56}}{{rp|57}}{{cite book | vauthors = Rapini RP, Bolognia JL, Jorizzo JL |title=Dermatology: 2-Volume Set |publisher=Mosby |location=St. Louis |year=2007 |isbn=978-1-4160-2999-1 }}

It was characterized in 1984.{{cite journal | vauthors = Torchia D, Miteva M, Hu S, Cohen C, Romanelli P | title = Papuloerythroderma 2009: two new cases and systematic review of the worldwide literature 25 years after its identification by Ofuji et al | journal = Dermatology | volume = 220 | issue = 4 | pages = 311–320 | date = March 2010 | pmid = 20339287 | doi = 10.1159/000301915 | s2cid = 23915213 }}{{cite journal | vauthors = Ofuji S, Furukawa F, Miyachi Y, Ohno S | title = Papuloerythroderma | journal = Dermatologica | volume = 169 | issue = 3 | pages = 125–130 | year = 1984 | pmid = 6148269 | doi = 10.1159/000249586 }}

Use of PUVA in treatment has been described.{{cite book| vauthors = Burg G, Kempf W |title=Cutaneous Lymphomas|url=https://books.google.com/books?id=xtm_H3u2QYAC&pg=PA365|access-date=30 May 2010|year=2005|publisher=Informa Health Care|isbn=978-0-8247-2997-4|pages=365–}}

See also

References

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