Immunodeficiency with hyperimmunoglobulin M

{{short description|Rare disorder}}

{{Infobox medical condition (new)

| name = {{PAGENAME}}

| synonyms = Hyper-IgM syndrome type 1{{cite web |title=X-linked hyper-IgM syndrome |url=https://www.orpha.net/consor/cgi-bin/OC_Exp.php?lng=en&Expert=101088 |website=Orphanet |access-date=18 March 2019}}

| image = X-linked recessive.svg

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| caption = This condition is inherited in an X-linked recessive manner

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| field = Medical genetics

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Immunodeficiency with hyperimmunoglobulin M is a rare disorder characterized by recurrent infections, low or absent IgG, IgE, and IgA levels, and normal or elevated levels of IgM and IgD.{{cite book |author1=James, William D. |author2=Berger, Timothy G. |title=Andrews' Diseases of the Skin: clinical Dermatology |publisher=Saunders Elsevier |year=2006 |isbn=978-0-7216-2921-6 |display-authors=etal}}{{rp|84}}